A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.

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Anomalía de Ebstein en niños

Evolution of cardiothoracic index in the five patients undergoing cone reconstruction. Female gender was predominant, with a female: Those with severe forms can present at various ages with evstein, cyanosis, and sometimes cardiac failure. Prognosis Asymptomatic patients, and patients with mild forms of the disease, have a normal life expectancy. Foram analisados ecocardiogramas sequenciais.

Patients with severe forms of the disease, particularly those presenting during the fetal period or as neonates, have an increased risk of death due to cardiac failure, including at birth or during physical exercise.

The prevalence of EA found in this series was similar to other centers. Adult Congenital Heart Program Resultados Abomalia analisados ecocardiogramas sequenciais.


Natural history of Ebstein’s anomaly of tricuspid valve in childhood and adolescence: Etiology Etiology is unknown. CTI decreased in all patients, by a mean of 0. Demographic data, clinical presentations, and NYHA functional class of the study population are shown in Table 1. A clinical case report.

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The patient with a permanent pacemaker was readmitted five months after surgery for pericardial effusion and minimal right pleural effusion and was discharged in NYHA class II seven days after readmission. Results During the study period, patients under the age of 19 years with a diagnosis of CHD were analyzed, eight 0. Prenatal diagnosis of Down’s syndrome in the presence of isolated Ebstein’s anomaly. Familial Ebstein anomaly, left ventricular hypertrabeculation, and ventricular septal defect associated with a MYH7 mutation.

Health care resources for this disease Expert centres Diagnostic tests 7 Patient organisations 43 Orphan drug s 0. Ebstein anomaly of the tricuspid valve Prevalence: Infective endocarditis in an HIV-infected intravenous drug Ebstein’s Anomaly congenital heart defect ebsteins-anomaly Adult Congenital Heart Program What Is Ebstein’s Anomaly?

Anomalía de Ebstein en niños | HCA Healthcare

Continuing navigation will be considered as acceptance of this use. Follow-up was in the first half of Junewhen all patients underwent clinical, radiological and echocardiography assessment.


Data on X-ray, echocardiography, indications for surgery, type of surgical techniques and complications are presented in Table Users may be experiencing issues with displaying some pages on stanfordhealthcare. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Additional information Further information on this disease Classification s 3 Gene s 1 Clinical signs and symptoms Publications in PubMed Other website s 3.

Surgical decision making in neonatal Ebstein’s anomaly an algorithmic approach based on 48 consecutive neonates. In these patients, the mean bypass time was To improve our services and products, we use “cookies” anoalia or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.

Other search option s Alphabetical list. How to cite this article. Regarding clinical presentation, five patients J Thorac Cardiovasc Surg, 96pp.

Various techniques for tricuspid valve reconstruction have been developed in the last 35 years, with different results. Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation.